© Springer Nature Switzerland AG 2021
C. S. Foster et al. (eds.)Uveitishttps://doi.org/10.1007/978-3-030-52974-1_71

71. Uveitis During Pregnancy

Jordan A. Ueberroth1  
(1)
Massachusetts Eye Research and Surgery Institution, Waltham, MA, USA
 
Keywords
UveitisPregnancy

Overview

  • Noninfectious uveitis in pregnancy shows increased disease activity early in pregnancy, significant reduction in activity in late trimesters, and rebound inflammation postpartum

  • Infectious uveitis, especially toxoplasma retinochoroiditis, may have a higher incidence of reactivation during pregnancy

  • When considering treatment, the risks and benefits to the fetus and mother must always be carefully weighed, with knowledge that severe, untreated inflammatory disease in the mother is possibly harmful to the fetus

Clinical Course

  • Hormonal changes in pregnancy ultimately decrease cell-mediated inflammation by upregulating Th2 cells and downregulating Th1 cells
    • These changes are driven by increased levels of estrogen, progesterone, alpha fetoprotein, cortisol, norepinephrine, prolactin, and 1,25-dihydroxyvitamin D

  • Improved disease activity in patients with Adamantiades-Behcet’s disease, VKH syndrome, sympathetic ophthalmia, HLA-B27 associated anterior uveitis, rheumatoid arthritis, juvenile idiopathic arthritis (JIA), and multiple sclerosis
    • There is notable inflammatory rebound in the 6 months after parturition

  • Potential worsening of systemic lupus erythematosus (SLE) disease activity

  • Rates of de novo infection and reactivation of toxoplasma retinochoroiditis are increased

  • Considerations for immunosuppression:
    • Although IMT carries risks, it is likely that untreated, severe disease also poses harm to the fetus

    • Non-infectious uveitis in pregnancy:
      • Prednisone and prednisolone (FDA Pregnancy Category B) are safe during pregnancy and breastfeeding
        • Dose exceeding 9 mg/day may be associated with fetal cleft palate and a theoretical risk of premature rupture of membranes or chorioamnionitis

      • Azathioprine (Category D) may be safely continued in pregnant women with severe disease at doses ≤2 mg/kg/day

      • Methotrexate, mycophenolate mofetil, and alkylating agents (Category X) are known teratogens and must be avoided in pregnancy and discontinued at least 3 months prior to conception

      • Tacrolimus and cyclosporine (Category C) are safe in low doses but should be avoided during breastfeeding

      • TNF-α inhibitors (Category B) appear to be safe and well-tolerated in pregnancy

      • Tocilizumab (Category C) and its effect on pregnancy have not been studied in humans

      • Rituximab (Category C) may cause neonatal B-cell lymphocytopenia and should be discontinued 1 year prior to conception

    • Infectious uveitis in pregnancy:
      • Toxoplasma retinochoroiditis:
        • Spiramycin 1 g TID is drug of choice during early pregnancy (<18 weeks gestation)
          • Significantly lowers vertical transmission rate

          • Licensed in Canada and Europe but available in the USA only directly through the FDA

        • Trimethoprim/sulfamethoxazole 160/800 mg BID can be used in late second or third trimester

      • Syphilitic uveitis:
        • Intravenous penicillin 18–24 million units/day for 2 weeks