Table 11.2 Improvements in Patient 1 after seven months of prednisone treatment

Month	CPK (lU/ml)	MVC (lbs)	T1 M	ATP (mmol-kg-1)	PCr (mmol-kg)	P/PCr ratio	Work/energy cost
1	4,962	15	1,890	4.2	13.6	0.49	7.1
7	63	40	1,265	6.9	23.6	0.31	32.3
Normal juvenile	30-210	32±5	1,083 ±26	6.6±0.3	25.5 ±1.2	0.27±0.02	29.9±5.3

Notes

Laboratory and metabolic values for Patient 1. Normal values are mean ± SEM for six healthy control subjects. T1 values are taken from VL.